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Differential diagnosis of small vessel cPACNS

Differential diagnosis of small vessel cPACNS
Nonvasculitic inflammatory brain diseases
Demyelinating inflammatory brain diseases (multiple sclerosis, ADEM)
Antibody mediated inflammatory brain diseases (anti-NMDAR encephalitis, limbic encephalitis, neuromyelitis optica, Hashimoto encephalitis, pediatric autoinflammatory neuropsychiatric disorder associated with streptococcal infections)
T cell parenchymal inflammatory brain diseases (Rasmussen encephalitis)
Granulomatous inflammatory brain diseases (neurosarcoidosis)
Infections
Tuberculosis
JC virus
Metabolic diseases
Mitochondrial encephalopathy lactic acidosis and stroke-like episodes (MELAS)
Rolandic mitochondrial encephalopathy (ROME)
Polymerase gamma deficiency
Malignancies
Angiocentric lymphoma
cPACNS: childhood primary angiitis of the central nervous system; ADEM: acute disseminated encephalomyelitis; NMDAR: N-methyl-D-aspartate receptor; JC: John Cunningham.
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