| Item | Sub-item(s) | Weight/score¶ |
| Skin thickening of the fingers of both hands extending proximal to the metacarpophalangeal joints (sufficient criterion) | – | 9 |
| Skin thickening of the fingers (only count the higher score) | Puffy fingers | 2 |
| Sclerodactyly of the fingers (distal to the metacarpophalangeal joints but proximal to the proximal interphalangeal joints) | 4 | |
| Fingertip lesions (only count the higher score) | Digital tip ulcers | 2 |
| Fingertip pitting scars | 3 | |
| Telangiectasia | – | 2 |
| Abnormal nailfold capillaries | – | 2 |
| Pulmonary arterial hypertension and/or interstitial lung disease (maximum score is 2) | Pulmonary arterial hypertension | 2 |
| Interstitial lung disease | 2 | |
| Raynaud phenomenon | – | 3 |
| SSc-related autoantibodies (anticentromere, anti-topoisomerase I [anti-Scl-70], anti-RNA polymerase III) (maximum score is 3) | Anticentromere Anti-topoisomerase I Anti-RNA polymerase III | 3 |
