| Percent with positive ANA |
Systemic autoimmune diseases |
SLE |
Active | 98 to 100 percent |
Remission | 90 percent |
Scleroderma | 95 percent |
Rheumatoid arthritis | 45 percent |
Sjögren's syndrome | 60 percent |
Mixed connective tissue disease | 100 percent |
Drug-induced LE | 80 to 95 percent |
Raynaud's phenomenon | 40 percent |
Polymyositis/dermatomyositis | 35 percent |
Juvenile idiopathic arthritis | 15 to 40 percent |
Organ-specific autoimmune diseases |
Hashimotos thyroiditis | 50 percent |
Graves' disease | 50 percent |
Autoimmune hepatitis | 70 percent |
Primary biliary cirrhosis | 50 to 70 percent |
Infectious diseases* |
Viral: |
EBV |
HIV |
HCV |
Parvovirus 19 |
Bacterial: |
SBE |
Syphilis |
Malignancies* |
Lymphoproliferative diseases |
Paraneoplastic syndromes |
Miscellaneous diseases* |
Inflammatory bowel disease |
Interstitial pulmonary fibrosis |