| Vertical gaze abnormalities, especially upgaze |
| Downward gaze preference or tonic downward deviation of the eyes ("setting-sun sign") |
| Primary position upbeat or downbeat nystagmus |
| Impaired convergence and divergence |
| Excessive convergence tone |
| Convergence-retraction nystagmus |
| Skew deviation, often with the higher eye on the side of the lesion |
| Alternating adduction hypertropia or alternating adduction hypotropia |
| Bilateral upper eyelid retraction (Collier "tucked-lid" sign) |
| Bilateral ptosis |
| Pupillary abnormalities (large with light-near dissociation) |
