| P | Posterior fossa brain malformations, most commonly the Dandy-Walker variant |
| H | Hemangiomas, particularly large, segmental facial lesions |
| A | Arterial anomalies |
| C | Cardiac anomalies and coarctation of the aorta |
| E | Eye abnormalities and endocrine abnormalities |
| S* | Sternal cleft, supraumbilical raphe, or both |
