Lipodystrophy |
Acanthosis nigricans (associated with severe hyperinsulinemia) |
Muscle hypertrophy, prominent veins |
Hepatomegaly |
Fatty liver |
Cirrhosis |
Hypertrichosis, hirsutism (occasionally) |
Cardiomegaly due to hypertrophic cardiomyopathy (occasionally) |
Developmental delay (occasionally) |
Metabolic abnormalities |
Hyperglycemia, but no ketosis |
Insulin resistance |
Hypertriglyceridemia |
Increased metabolic rate |