Criteria | Scoring system |
Clinical |
Basic | 2 points for basic criteria and two additional criteria |
Persistent and/or progressive patches/thin plaques | 1 point for basic criteria and one additional criterion |
Additional: | |
1. Non-sun-exposed location |
2. Size/shape variation |
3. Poikiloderma |
Histopathologic |
Basic | 2 points for basic criteria and two additional criteria |
Superficial lymphoid infiltrate | 1 point for basic criteria and one additional criterion |
Additional: | |
1. Epidermotropism without spongiosis |
2. Lymphoid atypia* |
Molecular biologic |
1. Clonal T cell receptor gene rearrangement | 1 point for clonality |
Immunopathologic |
1. <50% CD2+, CD3+, and/or CD5+ T cells | 1 point for one or more criteria |
2. <10% CD7+ T cells |
3. Epidermal/dermal discordance of CD2, CD3, CD5, or CD7¶ |