| Uhl anomaly | ARVC | |
| Family history | No | Yes (some patients) |
| Gender, ratio M:F | 1.3:1 | 2.9:1 |
| Age at presentation | Infancy + childhood | Adolescence + older |
| Usual mode of presentation | Heart failure | Arrhythmia, syncope, or sudden death |
| Exercise-induced deaths | Rare | Uncommon |
| Pathology | Areas of complete absence of myocardium of parietal wall of RV: endocardial and epicardial layers are directly opposed | Localized patchy replacement of the parietal wall of RV by fibrous and fatty tissue |
