Extrahepatic diseases | Frequency among patients with AIH (%) |
Pulmonary disorders | Fibrosing alveolitis | <1 |
Pulmonary fibrosis | <1 |
Sarcoidosis | <1 |
Asthma | 1 to 4 |
Hematological disorders | Immune thrombocytopenia | <1 |
Autoimmune hemolytic anemia | <1 |
Pernicious anemia | 1 |
Antiphospholipid syndrome | 1 |
Neurologic disorders | Multiple sclerosis | <1 |
Mononeuritis multiplex | <1 |
Miscellaneous | Primary amenorrhoea | 4 |
Glomerulonephritis | 1 |
Cryoglobulinemia | <1 |
Uveitis | <1 |
Polyglandular autoimmune syndrome | <1 |
Endocrine disorders | Autoimmune thyroiditis | 8 to 23 |
Diabetes (type 1) | 1 to 10 |
Gastrointestinal disorders | IBD (ulcerative colitis) | 2 to 8 |
Celiac disease +/– IgA deficiency | 1 to 6 |
Connective tissue disorders | Rheumatoid arthritis | 2 to 4 |
Sjögren's syndrome | 1 to 7 |
Mixed connective tissue disease | 1 to 2.5 |
Systemic lupus erythematosus | 1 to 2.6 |
Systemic sclerosis/scleroderma/CREST | <1 |
Polymyalgia rheumatica | <1 |
Polymyositis | <1 |
Dermatomyositis | <1 |
Skin disorders | Psoriasis | 3 |
Vitiligo | 1 to 2 |
Pyoderma gangrenosum | <1 |
Acne | <1 |
Urticaria | <1 |
Lichen planus | <1 |
Erythema nodosum | <1 |
Dermatitis herpetiformis | <1 |