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Causes of and risk factors for ischemic stroke in children and young adults

Causes of and risk factors for ischemic stroke in children and young adults
Cardiac
  • Congenital heart disease
  • Patent foramen ovale
  • Atrial septal aneurysm
  • Atrial myxoma
  • Atrial fibrillation
  • Other arrhythmia
  • Cardiomyopathy
  • Myocarditis
  • Myocardial infarction
  • Cardiac surgery
  • Cardiac catheterization
  • Extracorporeal membrane oxygenation (ECMO)
  • Endocarditis
  • Rheumatic heart disease
  • Prosthetic valve
Hematologic
  • Sickle cell disease
  • Inherited prothrombotic states:
    • Protein C deficiency
    • Protein S deficiency
    • Antithrombin deficiency
    • Factor V Leiden (associated with activated protein C resistance)
    • Prothrombin G20210A
    • Elevated homocysteine
    • Elevated lipoprotein(a)
    • Polycythemia vera
  • Acquired prothrombotic states:
    • Antiphospholipid syndrome
    • L-asparaginase
    • Pregnancy
    • Estrogen-containing contraceptives
    • Protein-losing enteropathy
    • Disseminated intravascular coagulation
    • Leukemia and other malignancies
Vascular
Noninflammatory
  • Arterial dissection:
    • Spontaneous
    • Traumatic
    • Secondary to connective tissue disease (Ehlers-Danlos, Marfan)
    • Fibromuscular dysplasia
  • Hypertension
  • Radiation vasculopathy
  • Moyamoya:
    • Primary moyamoya disease
    • Secondary moyamoya syndrome associated with:
      • Sickle cell disease
      • Neurofibromatosis type 1
      • Down syndrome
      • Williams syndrome
      • Cranial radiation
      • Fibromuscular dysplasia
      • Young women who smoke and use estrogen-containing contraceptives
      • Vasculitis and postinfectious vasculopathy
      • Viral or bacterial infection
      • Congenital heart disease
  • Vasospasm following subarachnoid hemorrhage
  • Congenital vessel hypoplasia
  • Migraine
Inflammatory
  • Focal cerebral arteriopathy
  • Takayasu arteritis
  • Giant cell arteritis
  • Kawasaki disease
  • Polyarteritis nodosa
  • Vasculitis associated with rheumatologic disease
  • Primary central nervous system angiitis
  • Infectious/postinfectious vasculitis:
    • Human Immunodeficiency Virus (HIV)
    • Varicella
    • Bacterial meningitis
    • Syphilis
    • Tuberculosis
    • Fungal
Metabolic
  • Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL)
  • Fabry disease
  • Homocystinuria
  • Menkes' disease
  • Mitochondrial encephalopathy with lactic acidosis and stroke-like episodes (MELAS)
Drug use
  • Cocaine
  • Methamphetamine
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