Manifestation | Frequency, percent |
Systemic symptoms | 80 |
Fever, malaise, weight loss |
Neuropathy | 75 |
Mononeuritis multiplex, polyneuropathy |
Arthralgias and/or myalgias | 60 |
Articular and/or diffuse extremity pain |
Cutaneous | 50 |
Livedo reticularis, purpura, ulcers |
Renal disease | 50 |
Elevated creatinine, hematuria, glomerulonephritis |
Gastrointestinal symptoms | 40 |
Abdominal pain, rectal bleeding |
Hypertension | 35 |
New onset |
Respiratory manifestations | 25 |
Infiltrates, nodules, cavities |
Central nervous system disease | 20 |
Stroke, confusion |
Orchitis | 20 |
Testicular pain, swelling |
Cardiac involvement | 10 |
Cardiomyopathy, pericarditis |
Peripheral vascular disease | 10 |
Claudication, ischemia, necrosis |