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Cobalamin metabolism

Cobalamin metabolism
Cbl: cobalamin; TC: transcobalamin; TCR: transcobalamin receptor; LMBRD1: KMBR1 domain-containing 1; ABCD4: ATP-binding cassette subfamily D member 4; HCFC1: host cell factor C1; MMACHC: methylmalonic aciduria and homocystinuria type C; MMADHC: methylmalonic aciduria and homocystinuria type D; MMAA: metabolism of cobalamin associated A; MMAB: metabolism of cobalamin associated B; AdoCbl: adenosylcobalamin; CoA: coenzyme A; MCEE: methylmalonyl-CoA epimerase; TCA: tricarboxylic acid; MTRR: 5-methyltetrahydrofolate-homocystein methyltransferase reductase.
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