Algorithm for the long-term management of catecholaminergic polymorphic ventricular tachycardia

CPVT: catecholaminergic polymorphic ventricular tachycardia; ICD: implantable cardioverter-defibrillator; AV: atrioventricular.
* We counsel patients with CPVT to avoid competitive sports and strenuous exercise.
¶ Long-acting, nonselective beta blockers (such as nadolol) are preferred over short-acting or B1 selective agents.
Δ Flecainide is contraindicated in patients with known structural heart disease (eg, coronary artery disease) or patients with high grade AV block or bifascicular block.
◊ Patients who have a high burden of arrhythmias or are intolerant of beta blockers should generally undergo sympathetic denervation.