Primary tumor (T) |
T category | T criteria |
TX | Primary tumor cannot be assessed |
T1 | PH <5 cm in greatest dimension, no extra-adrenal invasion |
T2 | PH ≥5 cm or PG-sympathetic of any size, no extra-adrenal invasion |
T3 | Tumor of any size with invasion into surrounding tissues (eg, liver, pancreas, spleen, kidneys) |
NOTE: Parasympathetic paragaglioma are not staged because they are largely benign. |
Regional lymph nodes (N) |
N category | N criteria |
NX | Regional lymph nodes cannot be assessed |
N0 | No lymph node metastasis |
N1 | Regional lymph node metastasis |
Distant metastasis (M) |
M category | M criteria |
M0 | No distant metastasis |
M1 | Distant metastasis |
M1a | Distant metastasis to only bone |
M1b | Distant metastasis to only distant lymph nodes/liver or lung |
M1c | Distant metastasis to bone plus multiple other sites |
Prognostic stage groups |
Pheochromocytoma/sympathetic paraganglioma |
When T is... | And N is... | And M is... | Then the stage group is... |
T1 | N0 | M0 | I |
T2 | N0 | M0 | II |
T1 | N1 | M0 | III |
T2 | N1 | M0 | III |
T3 | Any N | M0 | III |
Any T | Any N | M1 | IV |