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Branched-chain amino acid breakdown pathway

Branched-chain amino acid breakdown pathway
CoA: coenzyme A; BCKD: branched-chain ketoacid dehydrogenase.
* Regulatory enzymes: BCKD phosphatase and BCKD kinase.
Courtesy of Olaf A Bodamer, MD, PhD, FAAP, FACMG.
Graphic 106831 Version 1.0