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Differential diagnosis of recurrent oral ulcerations

Differential diagnosis of recurrent oral ulcerations
Rheumatologic diseases
  • Systemic lupus erythematosus
  • Reactive arthritis
Gastrointestinal diseases
  • Inflammatory bowel disease
  • Celiac disease
Autoinflammatory conditions
  • Periodic fever, aphthous stomatitis, pharyngitis and adenitis (PFAPA) syndrome
  • Hyperimmunoglobulinemia D syndrome
  • A20 haploinsufficiency
Infections
  • Herpes simplex virus
  • Human immunodeficiency virus
Dermatologic diseases
  • Stevens-Johnson syndrome
  • Pemphigoid
  • Pemphigus
  • Lichen planus
  • Linear IgA bullous dermatosis
Hematologic conditions
  • Cyclic neutropenia
Other
  • Drugs including methotrexate, other chemotherapy and nicorandil
  • Nutritional deficiencies such as vitamin B12, iron and folic acid
  • Recurrent aphthous stomatitis
Reprinted by permission from Macmillan Publishers Ltd: Nature Reviews Rheumatology. Ambrose NL, Haskard DO. Differential diagnosis and management of Behçet syndrome. Nat Rev Rheumatol 2013; 9:79. Copyright © 2013. www.nature.com/nrrheum.
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